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Tricuspid Atresia Tricuspid atresia is a rare congenital heart defect where a missing valve prevents blood from flowing between the right heart chambers, often resulting in an underdeveloped ventricle. To manage this and other single-ventricle conditions, patients typica
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Tricuspid atresia is a rare congenital heart defect where a missing valve prevents blood from flowing between the right heart chambers, often resulting in an underdeveloped ventricle. To manage this and other single-ventricle conditions, patients typically undergo a staged surgical sequence comprising the shunt, Glenn, and Fontan procedures. While the Fontan circulation successfully separates systemic and pulmonary blood flow, it creates a unique physiological state prone to long-term complications. These issues include arrhythmias, heart failure, and Fontan-associated liver disease, a condition involving universal liver fibrosis that can progress to cirrhosis. Current medical guidelines emphasize the necessity of multidisciplinary care teams and structured transitions from paediatric to adult specialist centres to manage these lifelong risks. Ongoing research into genetic factors and surgical risk factors continues to improve survival rates and refine the management of adult congenital heart disease.
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Erscheinungsdatum: 12.1.2026, 18:14:00
